Rare Forms of Cardiac Amyloidosis: Diagnostic Clues and Phenotype in Apo AI and AIV Amyloidosis.
Adam IoannouAldostefano PorcariRishi K PatelYousuf RazviGiulio SinigianiAna Martinez-NaharroLucia VenneriJames C MoonMuhammad Umaid RaufHelen LachmannAshutosh WechelakarPhilip N HawkinsJulian David GillmoreMarianna FontanaPublished in: Circulation. Cardiovascular imaging (2023)
Dysphonia, multisystem involvement, or right-sided cardiac disease should raise suspicion of AApoAI-CA. AApoAIV-CA presents most commonly with heart failure and always displays classical CA imaging features, mimicking common forms of CA. Both AApoAI and AApoAIV are associated with a good prognosis and a lower risk of mortality than matched patients with AL-amyloidosis.