The etiology of diffuse cystic lung diseases: an analysis of 1010 consecutive cases in a LAM clinic.
Han CuiChongsheng ChengWenshuai XuXinlun TianYanli YangYani WangJiannan HuangYudi HeJun WangRuie FengWeihong ZhangKai-Feng XuPublished in: Orphanet journal of rare diseases (2021)
Approximately 70% of DCLD patients in our LAM clinic had LAM. The common differential diagnoses included Birt-Hogg-Dubé syndrome, Sjogren's syndrome, and pulmonary Langerhans cell histiocytosis. Detailed clinical information and laboratory, genetic, and pathological investigations provide correct diagnoses in most patients with DCLD.