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Clinical, radiological, and pathological features of idiopathic and secondary interstitial pneumonia cases with pleuroparenchymal fibroelastosis undergoing lung transplantation.

Naoya IkegamiNaoki NakajimaAkihiko YoshizawaTomohiro HandaToyofumi Chen-YoshikawaTakeshi KuboKiminobu TanizawaAkihiro OhsumiYoshito YamadaMasatsugu HamajiDaisuke NakajimaYojiro YutakaSatona TanakaKizuku WatanabeYoshinari NakatsukaYuko MuraseTomoko NakanishiTakafumi NiwamotoKazuo ChinHiroshi DateToyohiro Hirai
Published in: Histopathology (2021)
Not all patients with interstitial pneumonia with radiological PPFE-like lesions have pathological PPFE. Characteristic clinical features can suggest the presence of pathological PPFE, and idiopathic and secondary cases with pathological PPFE are similar except for fibroblastic foci in idiopathic cases and alveolar septal thickening with elastosis or fibrosis in secondary cases. Patients with pathological PPFE have a similar prognosis to those with IPF after transplantation.
Keyphrases
  • heart failure
  • idiopathic pulmonary fibrosis
  • extracorporeal membrane oxygenation
  • mesenchymal stem cells
  • acute respiratory distress syndrome