Perioperative management of children with glycogen storage disease type II-Pompe disease.
Linelot BosmanSanne E HoeksAntonia González CandelHannerieke J M van den HoutAns T van der PloegLonneke M StaalsPublished in: Paediatric anaesthesia (2018)
Despite the potentially high anesthetic risk for children with Pompe disease under enzyme replacement therapy, the incidence of perioperative complications in our study was relatively low. Our data suggest that with proper precautionary measures and a critical choice of timing of the operation, general anesthesia in children with Pompe disease could be relatively safe nowadays.