Autoimmune Encephalitis Criteria in Clinical Practice.
Emma OrozcoCristina Valencia-SanchezJeffrey W BrittonDivyanshu DubeyEoin P FlanaganA Sebastian Lopez-ChiribogaNicholas ZalewskiAnastasia ZekeridouSean J PittockAndrew McKeonPublished in: Neurology. Clinical practice (2023)
The 2016 AE guidelines permit autoimmune causation assessment in subacute encephalopathy and are highly specific. Inclusion could be improved by incorporating AE-IgG-positive patients with isolated seizures or brainstem disorders. Some patients with atypical presentations but with findings supportive of autoimmunity may be immune therapy responsive.