Cystic Fibrosis Foundation Pulmonary Guidelines. Use of Cystic Fibrosis Transmembrane Conductance Regulator Modulator Therapy in Patients with Cystic Fibrosis.

Clement L RenRebecca L MorganChristopher M OermannHelaine E ResnickCynthia BradyAnnette CampbellRichard DeNagelMargaret GuillJeffrey HoagAndrew LiptonThomas NewtonStacy PetersDonna Beth Willey-CourandEdward T Naureckas

Published in: Annals of the American Thoracic Society (2019)

Using the GRADE approach, we have made recommendations for the use of CFTR modulators in patients with CF. These recommendations will be of help to CF clinicians, patients, and their families in guiding decisions regarding use of these medications.

Keyphrases

cystic fibrosis
pseudomonas aeruginosa
lung function
clinical practice
end stage renal disease
ejection fraction
newly diagnosed
chronic kidney disease
pulmonary hypertension
small molecule
palliative care
prognostic factors