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Clinical features and accompanying findings of Pseudo-Bartter Syndrome in cystic fibrosis.

Tugba Sismanlar EyubogluDeniz Dogru ErsozErkan CakirNazan CobanogluSevgi PekcanGuzin CinelEbru YalçınNural KiperVelat SenHadice Selimoglu SenOmur ErcanOzlem KeskinSevgi Bilgic EltanLina AlshadfanHakan YazanDerya Ufuk AltıntasAyse Senay SasihuseyinogluNihat SapanSükrü CekicHaluk CokugraşAyşe Ayzıt KılıncTugba Ramaslı GursoyAyse Tana AslanAysen BingolAbdurrahman Erdem BaşaranAli OzdemirMehmet KöseMelih HangulNagehan EmiralioğluGokçen TugcuHasan YukselOzge YılmazFazıl OrhanZeynep Gokce Gayretli AydınErdem TopalZeynep TamayAyse SuleymanDemet CanCem Murat BalGönül CaltepeUğur Ozcelik
Published in: Pediatric pulmonology (2020)
PBS was detected as the most common complication in the registry. It could be due to warm weather conditions of our country. It is usually seen in younger ages regardless of mutation phenotype and it could be a clue for early diagnosis of CF.
Keyphrases
  • cystic fibrosis
  • pseudomonas aeruginosa
  • lung function
  • case report
  • chronic obstructive pulmonary disease