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Common and Uncommon CT Findings in CVID-Related GL-ILD: Correlations with Clinical Parameters, Therapeutic Decisions and Potential Implications in the Differential Diagnosis.

Riccardo ScarpaFrancesco CinettoCinzia MilitoSabrina GianeseValentina SoccodatoHelena BusoGiulia GarziMaria CarrabbaEmanuele MessinaValeria PanebiancoCarlo CatalanoGiovanni MoranaVassilios LougarisNicholas LandiniMaria Pia Bondioni
Published in: Journal of clinical immunology (2023)
GL-ILD is a lower field predominant disease, commonly characterized by bronchiectasis, non-perilymphatic small nodules, consolidations, GGO and bands. Multiple small nodules, consolidations, reticulations and fibrotic ILD may suggest the presence of GL-ILD in CVID. MZ B cells percentage, IgA levels at diagnosis, lower field consolidations and mediastinal lymphnodes enlargement may predict the need of a specific GL-ILD therapy.
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