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Neurofibromatosis type-1-associated diffuse lung disease in children.

Paolo SpinnatoGiancarlo FacchiniCecilia TettaLudovica LotrecchianoMarco ColangeliAlberto BazzocchiUgo AlbisinniRenato CutreraPaolo TomàAlessandra Bartoloni
Published in: Pediatric pulmonology (2019)
Our research consolidates the hypothesis that diffuse lung disease is a direct manifestation of neurofibromatosis type-1 and that early onset is possible, even in pediatric patients.
Keyphrases
  • early onset
  • late onset
  • low grade
  • young adults