Spontaneous Pneumothoraces in Patients with Birt-Hogg-Dubé Syndrome.
Nishant GuptaElizabeth J KoprasElizabeth P HenskeLaura E JamesSouheil El-ChemalySrihari VeeraraghavanMatthew G DrakeFrancis X McCormackPublished in: Annals of the American Thoracic Society (2018)
Spontaneous pneumothorax is an important, recurrent manifestation of pulmonary involvement in patients with BHD, and pleurodesis should be considered following the initial pneumothorax to reduce the risk of recurrent episodes. In general, in patients with BHD, pneumothorax occurs in about 1-2 per 1,000 flights, and the risk is lower among patients with a history of prior pleurodesis.
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