Clinical and Prognostic Factors in Patients with IgG4-Related Kidney Disease.
Anis ChabaArnaud DevresseVincent AudardJean Jacques BoffaAlexandre KarrasClaire CarteryClément DeltombeJonathan M ChemounyClaudine ContaminCecille CourivaudSimon DuquennoyHugo GarciaDominique JolyNabila GoumriGuillaume HanounaJean-Michel HalimiEmmanuelle PlaisierMohamed HamidouCédric LandronDavid LaunayCeline LebasMathieu LegendreAgathe MasseauAlexis MathianLucile MercadalNathalie MorelPrisca Mutinelli-SzymanskiSylvain PalatJean-Loup PennaforteMarie Noelle PeraldiAgnieszka PozdzikNicolas SchleinitzOlivier ThaunatDimitri Titeca BeauportCharlotte MussiniSonia TouatiEric PrinzAnne Laure FallerSarah RichterEve VilaineSophie FerlicotClarissa Von-KotzeJulie BelliereJérôme OlagneRafik MesbahRenaud SnanoudjMathilde NouvierMikael EbboMohamad ZaidanPublished in: Clinical journal of the American Society of Nephrology : CJASN (2023)
IgG4-related kidney disease predominantly affected middle-aged males and manifested as tubulointerstitial nephritis with potential glomerular involvement. Complement consumption and the number of organs involved were associated with a higher relapse rate, whereas first-line therapy with Rituximab was associated with lower. Patients with high serum IgG4 concentrations (≥5g/L) had more severe kidney disease.