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Standard ECG for differential diagnosis between Anderson-Fabry disease and hypertrophic cardiomyopathy.

Giovanni VitaleRaffaello DitarantoFrancesca GrazianiIlaria TaniniAntonia CamporealeRosa LilloMarta RubinoElena PanaioliFederico Di NicolaValentina FerraraRossana ZanoniAngelo Giuseppe CaponettiFerdinando PasqualeMaddalena GraziosiAlessandra BerardiniMatteo ZiacchiMauro BiffiMarisa SantostefanoRocco LiguoriNevio TaglieriElena NardiAleš LinhartIacopo OlivottoClaudio RapezziElena Biagini
Published in: Heart (British Cardiac Society) (2021)
Standard ECG can help to differentiate AFD from HCM while investigating unexplained left ventricular hypertrophy. Short PR interval, prolonged QRS duration, RBBB, R in aVL ≥1.1 mV and inferior ST depression independently predicted AFD. Their systematic evaluation and the integration in a multiparametric ECG score can support AFD diagnosis.
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