Risk factors for mortality before age 18 years in cystic fibrosis.

Susanna A McColleyMichael S SchechterWayne J MorganDavid J PastaMarcia L CraibMichael W Konstan

Published in: Pediatric pulmonology (2017)

We identified multiple risk factors for childhood death of patients with CF, all of which remained important after incorporating FEV1 at age 6-8 years. Among the factors identified were the presence of clubbing or crackles at age 3-5 years, signs which are not routinely collected in registries.

Keyphrases

cystic fibrosis
pseudomonas aeruginosa
cardiovascular events
lung function
type diabetes
risk factors
coronary artery disease