Neurological Involvement in Childhood Evans Syndrome.
Thomas PincezBénédicte NevenHubert Ducou Le PointePascale VarletHelder FernandesAlbane GaretonGuy LevergerThierry LeblancHervé ChambostGérard MichelMarlène PasquetFrédéric MillotOlivier HermineAlexis MathianMarie HullyHélène ZephirMohamed HamidouJean-Marc DurandYves PerelJudith Landman-ParkerFréderic Rieux-LaucatNathalie AladjidiPublished in: Journal of clinical immunology (2019)
Neurological involvement is a rare and severe late event in the course of childhood ES, which can reveal an underlying PID. Imaging and pathology examination highlight a causative immune dysregulation that may guide targeted therapeutic strategies.