Login / Signup

Insights into phenotypic variability caused by GARS1 pathogenic variants.

Jesús Jiménez-JiménezIrene NavarreteInmaculada AzorínPilar MartíRoger VílchezNuria MuelasJavier Cabello-MurguiElvira MilletJuan Francisco Vázquez CostaJuan Jesus VilchezTeresa SevillaRafael Sivera
Published in: European journal of neurology (2024)
GARS1 variants may produce a dHMN phenotype with "split hand" and sensory disturbances, even when sensory nerve conduction studies are normal. This could be explained by a dysfunction of sensory neurons in the dorsal ganglion that is reflected as a reduction of dermal nerve endings in skin biopsies without a distal gradient.
Keyphrases
  • spinal cord
  • copy number
  • neuropathic pain
  • peripheral nerve
  • wound healing
  • oxidative stress
  • minimally invasive
  • ultrasound guided
  • optic nerve