Trends of vascular surgery procedures in Marfan syndrome and Ehlers-Danlos syndrome.
Senthil N JayarajanBrandon D DowningLuis A SanchezJeffrey JimPublished in: Vascular (2020)
Patients with Marfan syndrome and Ehlers-Danlos syndrome differ from other patients undergoing vascular surgical procedures, with a significantly higher proportion of aortic procedures including open aneurysm repair and thoracic endovascular aortic repair. While they are younger with fewer comorbidities, due to the unique pathogenesis of their underlying connective tissue disorder, there is an overall higher rate of procedural complications and increased length of stay and cost for Marfan syndrome patients undergoing aortic surgery.