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Left cardiac sympathetic denervation in children with Jervell Lange-Nielsen syndrome and drug refractory torsades - A case series.

Deepanjan BhattacharyaNarayanan NamboodiriMadhusoodanan Pillai SreelekshmiMukund Aravind PrabhuAbhilash Sreevilasam PushpangadhanSabarinath MenonBaiju S DharanAjitkumar Valaparambil
Published in: Pacing and clinical electrophysiology : PACE (2023)
Jervell Lange-Nielsen syndrome is a subtype of LQTS with high-risk features. LCSD, an effective therapeutic option for those having symptoms despite being on propranolol, results in significant reduction of QTc interval and amelioration of symptoms.
Keyphrases
  • young adults
  • sleep quality
  • left ventricular
  • heart failure
  • physical activity
  • adverse drug