Left cardiac sympathetic denervation in children with Jervell Lange-Nielsen syndrome and drug refractory torsades - A case series.
Deepanjan BhattacharyaNarayanan NamboodiriMadhusoodanan Pillai SreelekshmiMukund Aravind PrabhuAbhilash Sreevilasam PushpangadhanSabarinath MenonBaiju S DharanAjitkumar ValaparambilPublished in: Pacing and clinical electrophysiology : PACE (2023)
Jervell Lange-Nielsen syndrome is a subtype of LQTS with high-risk features. LCSD, an effective therapeutic option for those having symptoms despite being on propranolol, results in significant reduction of QTc interval and amelioration of symptoms.