Serial assessments of anterior pituitary hormones in a case of mixed histiocytosis representing Langerhans cell histiocytosis overlapping with Erdheim-Chester disease.
Kei ItoJun ItoYuki YamamotoRikako NakajimaMasanao FujiiYukino KatakuraAiko MuramatsuNorio TakayashikiKazuhiro ToyamaMineo KurokawaHiroaki YagyuPublished in: Endocrinology, diabetes & metabolism case reports (2021)
Erdheim-Chester disease and Langerhans cell histiocytosis overlapping as MH was described, focusing on pituitary functions. MH caused both GH deficiency and central diabetes insipidus. Despite a lack of radical therapy for MH, no other anterior pituitary dysfunctions emerged for 2 years. Radiological images showed no particular interval changes in pituitary stalk lesions, while vascular and retroperitoneal involvements extended.