Echocardiographic diagnosis of Shone's syndrome.
Xin ZhangGuiqin MaLin ZhengHongju ZhangYan SunJingya LiNing MaPublished in: Echocardiography (Mount Kisco, N.Y.) (2020)
Shone's syndrome is a rare congenital heart disease that includes 4 cardiovascular anomalies: supravalvular mitral ring, parachute mitral valve, subaortic stenosis, and coarctation of the aorta. Early diagnosis and treatment result in better outcomes. Echocardiography plays an important role in the diagnosis and is the optimal examination for detecting this disease. Pressure gradients are often unreliable and inaccurate; thus, careful anatomical observation of the left ventricular inflow and outflow tracts, particularly the mitral valve, is vital for accurate diagnosis and planning appropriate management. Herein, we describe 9 cases of Shone's syndrome, diagnosed with echocardiography and treated surgically.
Keyphrases
- mitral valve
- left ventricular
- left atrial
- congenital heart disease
- aortic stenosis
- acute myocardial infarction
- hypertrophic cardiomyopathy
- cardiac resynchronization therapy
- heart failure
- pulmonary hypertension
- case report
- computed tomography
- aortic valve
- insulin resistance
- acute coronary syndrome
- adipose tissue
- newly diagnosed