Improved Nutritional Outcomes and Gastrointestinal Symptoms in Adult Cystic Fibrosis Patients Treated with Elexacaftor/Tezacaftor/Ivacaftor.
Nela StastnaLumir KunovskyMichal SvobodaEva PokojovaLukas HomolaMiriam MalaZaneta GracovaBarbora JerabkovaJana SkrickovaJan TrnaPublished in: Digestive diseases (Basel, Switzerland) (2024)
Our data suggest increased nutritional parameters, lower pancreatic substitution requirements, and improved defecation in adult CF patients on ETI. Improvement in exocrine pancreatic function might be mutation-specific and needs further study.
Keyphrases
- cystic fibrosis
- end stage renal disease
- pseudomonas aeruginosa
- newly diagnosed
- ejection fraction
- lung function
- chronic kidney disease
- prognostic factors
- peritoneal dialysis
- electronic health record
- big data
- type diabetes
- machine learning
- sleep quality
- skeletal muscle
- patient reported outcomes
- deep learning
- air pollution
- weight loss
- patient reported