Clinical course of suspected familial and sporadic idiopathic pulmonary fibrosis: Data from the PROOF-Next registry.

Antoine FroidureBenjamin BondueCaroline DahlqvistJulien GuiotNatacha GusbinGil WirtzGuy G O BrusselleDanielle StrensHans SlabbynckWim A Wuyts

Published in: Respirology (Carlton, Vic.) (2023)

Although younger and exposed to less tobacco, patients with FPF show an equally aggressive progression as observed in sporadic IPF patients. These results warrant early referral of FPF patients to expert centres for optimal management.

Keyphrases

idiopathic pulmonary fibrosis
end stage renal disease
newly diagnosed
ejection fraction
prognostic factors
peritoneal dialysis
early onset
big data
deep learning
artificial intelligence
patient reported