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The Update of Treatment for Primary Intestinal Lymphangiectasia.

Yiyoung KwonMi-Jin Kim
Published in: Pediatric gastroenterology, hepatology & nutrition (2021)
Intestinal lymphangiectasia is a rare disease which is causing protein-losing enteropathy. Treatment of intestinal lymphangiectasia can be a challenge for clinicians because of the lack of specific guidelines regarding pharmacological indications. We sought to introduce a diagnostic approach and suggest guidelines for treatment. After exclusion of secondary intestinal lymphangiectasia, magnetic resonance lymphangiography is a promising tool for the assessment of abnormal lymphatic lesions in primary intestinal lymphangiectasia. Determining the extent of the lesion provides direction for treatment options. Focal short-segment intestinal lymphangiectasia can be treated via intestinal resection or radiologic embolization after dietary therapy failure. Diffuse intestinal lymphangiectasia and extensive lymphangiectasia should be treated with several drugs with a full understanding of their mechanisms.
Keyphrases
  • magnetic resonance
  • stem cells
  • magnetic resonance imaging
  • computed tomography
  • clinical practice
  • mesenchymal stem cells
  • palliative care
  • small molecule
  • low grade