Reduced risk of recurrent pneumothorax for sirolimus therapy after surgical pleural covering of entire lung in lymphangioleiomyomatosis.
Teiko SakuraiToru AraiMasaki HiroseKensuke KojimaTetsuki SakamotoYoshinobu MatsudaChikatoshi SugimotoHyung-Eun YoonYoshikazu InouePublished in: Orphanet journal of rare diseases (2021)
We first reported sirolimus might effectively suppress the recurrence of pneumothoraces in LAM patients who received SPC. Sirolimus induction after SPC (TPC or mTPC) might be a feasible option for frequent pneumothorax in LAM.