Clinical, biological, prognostic characteristics of patients with immune-mediated thrombotic thrombocytopenic purpura and Sjögren's disease.
Justine LucianoLaurent GilardinGaetane NocturneRaïda BouzidAgnès VeyradierXavier MariettePaul CoppoIsabelle BonnetBérangère S JolyPublished in: RMD open (2024)
iTTP can be a rare complication in patients with SjD. Further studies involving larger cohorts and long-term follow-up are warranted to confirm these findings and to explore the efficacy of immunomodulators and caplacizumab in iTTP-SjD patients.