'Hot phase' clinical presentation in arrhythmogenic cardiomyopathy.
Riccardo BarianiAlberto CiprianiStefania RizzoRudy CeleghinMaria Bueno MarinasBenedetta GiorgiMonica De GaspariIlaria RigatoLoira LeoniAlessandro ZorziManuel De LazzariAlessandra RampazzoSabino IlicetoGaetano ThieneDomenico CorradoKalliopi PilichouCristina BassoMartina Perazzolo MarraBarbara BaucePublished in: Europace : European pacing, arrhythmias, and cardiac electrophysiology : journal of the working groups on cardiac pacing, arrhythmias, and cardiac cellular electrophysiology of the European Society of Cardiology (2021)
'Hot phase' represents an uncommon clinical presentation of AC, which often occurs in paediatric patients and carriers of desmoplakin gene mutations. Tissue characterization, family history, and genetic test represent fundamental diagnostic tools for differential diagnosis.