Comparison of sporadic and FAP-associated desmoid-type fibromatoses.
Laura E KoskenvuoAri RistimäkiAnna LepistöPublished in: Journal of surgical oncology (2017)
The predictors for FAP occurrence among desmoid tumor patients are large tumor size, intra-abdominal location, multiple tumors, and patient's young age. Desmoid-type fibromatosis patients suffer a high recurrence rate, also among those experiencing sporadic tumors, but the risk of death due to the tumor is low. Conversely, desmoid disease represents a substantial cause of death among FAP patients.