Occurrence of focal myositis during Behçet's disease: the identification of a specific vasculitis-associated focal myopathy.

Laure GallayArnaud HotYves AllenbachDelphine Maucort-BoulchCloe ComarmondCindy MarquesLaurent PerardAnne SimonKuberaka MariampillaiPatrice CacoubLaure Mery-BossardPascal CathebrasLeonard FeassonAlice BerezneChafika MoratiLola LessardMarie FaruchNathalie StreichenbergerDavid Saadounnull null

Published in: Neuropathology and applied neurobiology (2023)

FM occurring during BD appears to be part of the systemic vasculitis process, and presents as a vasculitis-associated focal myopathy with a specific clinico-histological pattern. Patients with this association require long-term follow-up and adapted management. This case series also highlights the need for research on BD diagnostic criteria in cases of FM.

Keyphrases

late onset
risk assessment
muscular dystrophy
interstitial lung disease
early onset
rheumatoid arthritis
systemic sclerosis
drug induced
idiopathic pulmonary fibrosis