Derivation and validation of four patient clusters in Still's disease, results from GIRRCS AOSD-study group and AIDA Network Still Disease Registry.
Roberto CaporaliFrancesco MaseduAntonio VitaleIlenia Di ColaValeria CaggianoClaudia Di MuzioPaola CiprianiMarco ValentiOnorina BerardicurtiLuca NavariniDaniela IaconoIlenia PantanoDaniele MauroFrancesco CicciaSilvia RossiLudovico De StefanoSara MontiSerena BugattiCarlomaurizio MontecuccoFrancesco CasoLuisa CostaMarcella PreteFederico PerosaAnnamaria IagnoccoFabiola AtzeniGiuliana GugginoHenrique Ayres Mayrink GiardiniIsabele Parente de Brito AntonelliIbrahim A AlmaghlouthKazi Nur AsfinaRafi Haner DireskeneliFatma Alibaz-OnerGizem SevikAbdurrahman TufanPetros P SfikakisFrancesco La TorreAndrea Hinojosa-AzaolaEduardo Martín-NaresJiram Torres-RuizGafaar RagabMaria Cristina MaggioJoanna MakowskaEmanuela Del GiudiceElena BartoloniGiacomo EmmiMarcello GovoniAlberto Lo GulloGiuseppe LopalcoGabriele SimoniniLampros FotisBenson OgunjimiSamar TharwatBruno FredianiArmin MaierFrancesco CarubbiLorenzo DagnaSukran ErtenAntonio GidaroJosé Hernández-RodríguezPaolo SfrisoClaudia FabianiRoberto GiacomelliClaudia FabianiPublished in: RMD open (2023)
Four patient clusters in Still's disease may be recognised by a multidimensional characterisation ('Juvenile/Transitional', 'Uncomplicated', 'Hyperferritinemic' and 'Catastrophic'). Of interest, cluster 4 was burdened by an increased rate of life-threatening complications and mortality, suggesting a more severe patient group.