Susac syndrome (Retino-cochleo-cerebral vasculitis), the ophthalmologist in the role of the whistleblower.
Ioannis PapasavvasBarbara TeuchnerCarl Peter HerbortPublished in: Journal of ophthalmic inflammation and infection (2020)
Susac syndrome is a multilocation arteritis of the head that can involve the eye, ear and brain often first diagnosed by the ophthalmologist. The diagnosis is rapidly reached in uveitis referral centres but seems to be missed otherwise, A helpful angiographic sign to be searched is an abrupt or segmental arterial stop and increased staining of the arterial wall more clearly seen on indocyanine green angiography. Patients often present first to the ophthalmologist who should be acting as a whistleblower to avoid severe involvement of the brain.
Keyphrases
- resting state
- newly diagnosed
- ejection fraction
- white matter
- end stage renal disease
- primary care
- case report
- cerebral ischemia
- computed tomography
- optical coherence tomography
- prognostic factors
- subarachnoid hemorrhage
- early onset
- juvenile idiopathic arthritis
- functional connectivity
- rheumatoid arthritis
- ankylosing spondylitis
- patient reported outcomes
- optic nerve
- disease activity