Clinical predictors and explant lung pathology of acute exacerbation of idiopathic pulmonary fibrosis.
Yaniv DotanWilliam B ShapiroEneida MaleEduardo C DominguezAmandeep AnejaHuaqing ZhaoChandra DassKartik ShenoyNathaniel MarchettiFrancis C CordovaGerard J CrinerA James MamaryPublished in: ERJ open research (2020)
Lung transplantation candidacy testing including reflux studies did not predict AE-IPF besides FVC absolute decline. CT did not predict clinical or pathological AE-IPF. Secondary diverse lung pathology beyond diffuse alveolar damage was present in most AE-IPF, but not in stable IPF.
Keyphrases
- idiopathic pulmonary fibrosis
- interstitial lung disease
- chronic obstructive pulmonary disease
- computed tomography
- liver failure
- respiratory failure
- oxidative stress
- extracorporeal membrane oxygenation
- magnetic resonance
- low grade
- magnetic resonance imaging
- intensive care unit
- contrast enhanced
- drug induced
- image quality
- hepatitis b virus
- aortic dissection
- dual energy
- high grade