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Effectivenesss of ivacaftor in severe cystic fibrosis patients and non-G551D gating mutations.

Donatello SalvatoreVincenzo CarnovalePaola IacotucciCesare BraggionCarlo CastellaniGiuseppe CiminoCarmela ColangeloMichela FrancalanciGiuseppina LeonettiVincenzina LucidiAntonio MancaPamela VitulloNicola Ferrara
Published in: Pediatric pulmonology (2019)
Ivacaftor was safe and effective in patients with CF with severe lung disease and non-G551D gating mutations.
Keyphrases
  • cystic fibrosis
  • pseudomonas aeruginosa
  • end stage renal disease
  • lung function
  • ejection fraction
  • newly diagnosed
  • chronic kidney disease
  • early onset
  • peritoneal dialysis
  • prognostic factors