Anaplastic sarcoma of the kidney (DICER1-sarcoma of the kidney): A report from the International Pleuropulmonary Blastoma/DICER1 Registry.
Peter J SchoettlerCaroline C SmithMiki NishitaniAnne K HarrisAlexander T NelsonDave A WatsonJunne KamiharaElizabeth A MullenD Ashley HillYoav H MessingerDouglas B FairKiran A KumarLouis P DehnerShifra AshKenneth S ChenKris Ann P SchultzPublished in: Pediatric blood & cancer (2024)
ASK is a rare DICER1-related renal neoplasm. In the current report, we identify clinical and treatment-related factors associated with outcome including the importance of chemotherapy in treating ASK. Ongoing data collection and genomic analysis are indicated to optimize outcomes for children and adults with these rare tumors.