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Respiratory muscle weakness in facioscapulohumeral muscular dystrophy.

Carolin HenkeJens SpiesshoeferHans-Joachim KabitzSimon HerkenrathWinfried RanderathTobias BrixDennis GörlichPeter YoungMatthias Boentert
Published in: Muscle & nerve (2019)
In FSHD, respiratory muscle weakness involves both the diaphragm and the expiratory abdominal muscles.
Keyphrases
  • muscular dystrophy
  • skeletal muscle
  • duchenne muscular dystrophy
  • mechanical ventilation
  • respiratory tract
  • intensive care unit