EPIDEMIOLOGY AND GEOGRAPHIC CLUSTERING OF ERDHEIM-CHESTER DISEASE IN ITALY AND FRANCE.
Francesco PeyronelJulien HarocheCampochiaro CorradoFrancesco PegoraroZahir AmouraAlessandro TomelleriMartina MazzariolMatthias PapoGiulio CavalliGiuseppe Daniele BenignoParide FenaroliChrysanthos GrigoratosMaria Cecilia MengoliArturo BonomettiEmilio BertiGustavo SavinoMauro CivesIria NeriGaetano PacinellaAntonino TuttolomondoMassimo MaranoFrancesco MuratoreAndreina ManfrediAlessandro BroccoliPier Luigi Luigi ZinzaniBiagio DidonaChiara MassaccesiAndrea BuonoEnrico AmmiratiVito Di LerniaLorenzo DagnaAugusto VaglioFleur Cohen-AubartPublished in: Blood (2023)
In this geo-epidemiological study performed in Italy-France, Erdheim-Chester disease (ECD) is increasingly diagnosed in the past few years and cases cluster in specific geographic areas, namely Southern Italy and Central France. Disease frequency inversely correlates with the Human Development Index.
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