Ebstein's Anomaly, Left Ventricular Noncompaction and Gerbode-Like Defect Triad (Fetal Diagnosis and Neonatal Course).
Mohammad MehdiSnigdha BhatiaMehul PatelAshraf M AlyPublished in: Case reports in pediatrics (2021)
Ebstein's anomaly is characterized by the apical displacement of the septal and posterior leaflets of the tricuspid valve with atrialization of the right ventricle (RV). It is commonly associated with other heart defects including left ventricular noncompaction. We describe a case of prenatally diagnosed Ebstein's anomaly in association with left ventricular noncompaction and a septal defect between the left ventricle and the atrialized portion of the RV (Gerbode-like defect). The patient underwent a modified Blalock-Taussig shunt followed by Glenn procedure because of severe RV hypoplasia and RV outflow tract obstruction. The patient tolerated both procedures and is doing clinically well in anticipation of Fontan procedure for single ventricle palliation.
Keyphrases
- mitral valve
- left ventricular
- mycobacterium tuberculosis
- hypertrophic cardiomyopathy
- aortic stenosis
- left atrial
- pulmonary artery
- heart failure
- case report
- cardiac resynchronization therapy
- acute myocardial infarction
- pulmonary hypertension
- minimally invasive
- aortic valve
- transcatheter aortic valve replacement
- ejection fraction
- coronary artery
- drug induced
- acute coronary syndrome
- percutaneous coronary intervention