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Bilateral Sensorineural Hearing Loss Related to a Skull Base Spontaneous Cerebrospinal Fluid Leak: A Case Report and Literature Review.

Lorenzo Maria GainiLudovica BattilocchiGiorgio ConteMichele GaffuriDiego ZanettiLorenzo PignataroSara Torretta
Published in: Ear, nose, & throat journal (2023)
Spontaneous intracranial hypotension (SIH) is a rare condition characterized by orthostatic headache, pulsatile tinnitus, vertigo, nausea, and fluctuating hearing loss; this latter seems to be due to the development of cochlear endolymphatic hydrops following negative cerebrospinal fluid (CSF) pressure transmitted to the perilymphatic space through a patent cochlear aqueduct. We here describe a case of bilateral progressive sensorineural hearing loss (SNHL) due to intracranial hypotension caused by an undiagnosed spontaneous CSF leak from a skull base defect in a middle-aged woman. To the best of our knowledge, this is the first report describing a SNHL in a patient affected by SIH secondary to sphenoidal CSF leak.
Keyphrases
  • cerebrospinal fluid
  • hearing loss
  • case report
  • middle aged
  • multiple sclerosis
  • healthcare
  • optic nerve