Characteristics and Outcomes of Patients with Systemic Lupus Erythematosus-associated Thrombotic Microangiopathy, and Their Acquired ADAMTS13 Inhibitor Profiles.
Cai YueJian SuRuitong GaoYubing WenChao LiGang ChenXuan ZhangXuemei LiPublished in: The Journal of rheumatology (2018)
Acquired ADAMTS13 deficiency is associated with more severe thrombocytopenia and CNS involvement, mild renal involvement, rapid resolution, and relatively good treatment response in SLE-associated TMA.