Liver Transplantation for Nijmegen Breakage Syndrome With Hepatic Malignancy and Hepatopulmonary Syndrome After Bone Marrow Transplantation: A Case Report.
Oğuzhan ŞalMehmet Fatih ErbeyAyşe ArmutluGülsün KarasuBarış DemirNuray Uslu KızılkanAkın AkbulutTuran KanmazAltan AlimPublished in: Pediatric transplantation (2024)
NBS patients have an increased prevalence of malignancies, including primary hepatic malignancy, but most are managed medically or with limited resections. Transplantation in these patients can be curative for hepatic malignancy with a favorable safety profile.