Multimodality imaging of Abernethy malformation.
Ahmed Y El-MedanyGui RegoMatthew WilliamsStephen LyenMark TurnerPublished in: Echocardiography (Mount Kisco, N.Y.) (2022)
Abernethy malformation, or congenital extrahepatic portosystemic venous shunt, is a rare anomaly involving the portal venous system. Despite its rarity, it is increasingly being reported, and therefore, it is important to diagnose given the potential adverse clinical consequences if left untreated. It has a spectrum of presentations, ranging from complete lack of symptoms, to causing hepatic carcinoma, hepatic encephalopathy, severe pulmonary hypertension, and diffuse pulmonary arteriovenous malformation. We herein describe the case and echocardiographic, computed tomography, and magnetic resonance imaging findings of a transgender individual, with this anomaly detected incidentally during adulthood.
Keyphrases
- pulmonary hypertension
- pulmonary artery
- computed tomography
- magnetic resonance imaging
- early onset
- pulmonary arterial hypertension
- high resolution
- contrast enhanced
- positron emission tomography
- low grade
- sleep quality
- magnetic resonance
- left ventricular
- heart failure
- risk assessment
- hepatitis c virus
- dual energy
- physical activity
- early life
- drug induced
- adverse drug
- mass spectrometry
- image quality
- high grade
- climate change
- atrial fibrillation