Paraneoplastic pemphigus associated with Castleman disease: A multicenter case series.
Kelly K BarryIsabella PlumptreChristopher G BazewiczBrian P GreenJames R TreatMeagan HughesKimberly D MorelKaren WissMarilyn G LiangPublished in: Pediatric dermatology (2022)
Most patients had UCD, and the retroperitoneum was the most common location. Patients with MCD, incomplete resection, and BO died; patients with UCD and complete resection remain alive, even in the setting of BO. Consideration of PNP is critical when pediatric patients present with mucositis as PNP may be clinically indistinguishable from more common causes of mucositis.