Prognostic factors of adult hemophagocytic lymphohistiocytosis and clinical utility of HLH-2004 diagnostic criteria and HScore: A real-world multicenter study from Thailand.
Pitchayaporn JongdeeJakrawadee JulamaneeEkarat RattarittamrongSarita MukuraChinadol WanitpongpunRawisut DeoisaresAnoree SurawongThunyamon ChajuwanChantiya ChanswangphuwanaPublished in: Acta haematologica (2024)
Ferritin is a helpful biomarker for HLH diagnosis and prognostic prediction. Autoimmune disease triggered HLH has favorable outcomes. Future prospective study is required to verify use of the adapted HLH-2004 criteria.