Unique manifestation of a multifocal adult rhabdomyoma involving the soft palate-case report and review of literature.
Michael DauStine-Kathrein KraeftPeer Wolfgang KämmererPublished in: Journal of surgical case reports (2019)
Extracardiac adult rhabdomyoma is a rare benign tumor, which mainly occurs in the head and neck region and originates from striated muscle tissue. We report a 64-year-old male with simultaneous diagnosis of three adult rhabdomyomas including the soft palate and performed a review the literature on multifocal adult rhabdomyoma (mARM). Including the present case, 27 mARM with a range of 2-7 lesions per patient were collected. Mean age at diagnosis was 65 years with a male (23) to female (4) ratio of 5.75:1. Common localizations were parapharyngeal space (35%), larynx (14%), submandibular (13%), paratracheal region (14%), tongue (10%), floor of mouth (9%), neck (3%) and soft palate (2%). In accordance to this review, this the first case of mARM with involvement of the soft palate.