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Dermatomyofibroma-A rare mesenchymal tumor with maintained horripilation.

Uwe WollinaJacqueline Schönlebe
Published in: Dermatologic therapy (2019)
Dermatomyofibroma is a rare mesenchymal tumor of skin. The major differential diagnosis is dermatofibrosarcoma protuberans. Both lesions are composed of spindle-shaped cells which are CD34-positive. In contrast to the malignant counterpart, the tumor cells in dermatomyofibroma are without any evidence of COL1A1-PDGFB gene rearrangement. We present a case of axillary dermatomyofibroma in a 31-year-old woman. A hitherto undescribed clinical phenomenon is a maintained horripilation in contrast to dermatofibrosarcoma protuberans.
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