Dermatomyofibroma-A rare mesenchymal tumor with maintained horripilation.

Dermatomyofibroma is a rare mesenchymal tumor of skin. The major differential diagnosis is dermatofibrosarcoma protuberans. Both lesions are composed of spindle-shaped cells which are CD34-positive. In contrast to the malignant counterpart, the tumor cells in dermatomyofibroma are without any evidence of COL1A1-PDGFB gene rearrangement. We present a case of axillary dermatomyofibroma in a 31-year-old woman. A hitherto undescribed clinical phenomenon is a maintained horripilation in contrast to dermatofibrosarcoma protuberans.