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Progressive subglottic stenosis in a child with Pallister-Killian syndrome.

Tadashi ShiohamaKatsunori FujiiKenji ShimizuHirofumi OhashiTomozumi TakataniNobuhiko OkamotoGen NishimuraMitsuhiro KatoNaoki Shimojo
Published in: Congenital anomalies (2017)
Pallister-Killian syndrome (PKS) is rare genetic disorder caused by tetrasomy 12p mosaicism with supernumerary isochromosome 12p that manifests with intellectual disability, craniofacial dysmorphism, and epilepsy. Although PKS presents as a multisystem morphological defect, respiratory system involvement is rare, except for diaphragmatic hernia. We are the first to report a case of PKS with progressive subglottic stenosis. Subglottic stenosis is a potentially lethal condition due to severe respiratory obstruction and difficult intubation; therefore, further accumulation of cases is required to assess the causal link between PKS and subglottic stenosis.
Keyphrases
  • intellectual disability
  • multiple sclerosis
  • autism spectrum disorder
  • mental health
  • cardiac arrest
  • genome wide
  • dna methylation
  • respiratory tract