Efficacy and safety of low-dose Sirolimus in Lymphangioleiomyomatosis.

Hee-Young YoonJung Jin HwangDong Soon KimJin Woo Song

Published in: Orphanet journal of rare diseases (2018)

Low-dose sirolimus may stabilise lung function decline in lymphangioleiomyomatosis patients, but its efficacy appears to be inferior to that of conventional-dose sirolimus.

Keyphrases

low dose
lung function
end stage renal disease
high dose
cystic fibrosis
newly diagnosed
chronic obstructive pulmonary disease
ejection fraction
chronic kidney disease
prognostic factors
peritoneal dialysis