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Rescue of respiratory failure in pulmonary alveolar proteinosis due to pathogenic MARS1 variants.

Dominic LenzMirjam StahlElias SeidlDominik SchöndorfHeiko BrennenstuhlFlorian GesenhuesTina HeinzmannThomas LongerichMarisa I MendesHolger ProkischGajja S SalomonsCarola SchönDesirée E C SmithOlaf SommerburgMatias WagnerJens H WesthoffKarl ReiterChristian StaufnerMatthias Griese
Published in: Pediatric pulmonology (2020)
Catabolic events can provoke a severe deterioration of the pulmonary situation in ILLD with a need for repetitive WLL. Although the precise role of oral methionine supplementation and high protein intake are unknown, we observed an apparent treatment benefit, which needs to be evaluated systematically in controlled trials.
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