[Clinical case of generalized amyloidosis (ATTR-amyloidosis) with a progressive course of chronic heart failure. Case report].
D P GolubovskayaE V Dren'A V YurkinaT B PecherinaOlga L BarbarashPublished in: Terapevticheskii arkhiv (2024)
Despite the presence of various signs of cardiac amyloidosis ("red flags"), the introduction into routine practice of new non-invasive diagnostic methods (Speckle Tracking technology using echocardiography, myocardial scintigraphy with technetium pyrophosphate, genetic testing, screening for free light chains of immunoglobulins to exclude AL-amyloidosis), which have high specificity and sensitivity, transthyretinic (ATTR) cardiomyopathy is still a difficult to diagnose disease, especially in the early stages when treatment is most effective. The article presents a clinical case of ATTR-amyloidosis with predominant heart damage, manifested by severe diastolic heart failure resistant to treatment. The timing, from the moment of the first episode of decompensation of heart failure to death, is 4 months, which confirms the rapid progression of severe biventricular dysfunction of the heart. Despite the presence of cardiac and extracardial "red flags" of ATTR-amyloidosis in the patient, the diagnosis was established at autopsy. The paper analyzes possible errors of early diagnosis at the outpatient and inpatient stages of patient management.
Keyphrases
- heart failure
- left ventricular
- case report
- multiple myeloma
- cardiac resynchronization therapy
- atrial fibrillation
- healthcare
- oxidative stress
- primary care
- multiple sclerosis
- blood pressure
- early onset
- emergency department
- acute heart failure
- patient safety
- combination therapy
- quality improvement
- replacement therapy
- adverse drug
- loop mediated isothermal amplification