Epidemiology of paraneoplastic neurological syndromes: a population-based study.
Alberto VogrigGian Luigi GigliSamantha SegattiElisa CorazzaAlessandro MariniAndrea BernardiniFrancesca ValentMartina FabrisFrancesco CurcioFrancesco BrigoDonatella IaconoPaolo PassadoreMichele RanaJérôme HonnoratMariarosaria ValentePublished in: Journal of neurology (2019)
This first population-based study found an incidence of PNS that approximates 1/100,000 person-years and a prevalence of 4/100,000. Moreover, the incidence of PNS is increasing over time, probably due to increased awareness and improved detection techniques.