Imaging findings of COPA Syndrome.
HaiThuy N NguyenRida SalmanTiphanie P VogelManuel Silva-CarmonaMarietta DeGuzmanR Paul GuillermanPublished in: Pediatric radiology (2023)
The most prevalent imaging finding of COPA syndrome is diffuse lung disease related to early childhood-onset recurrent pulmonary hemorrhage and lymphoid hyperplasia that may progress to pulmonary fibrosis. Other imaging findings manifesting later in childhood or adolescence relate to arthritis and glomerulonephritis.