Free carnitine and branched chain amino acids are not good biomarkers in Huntington's disease.
Raphael Machado do CastilhosMarina Coutinho AugustinJosé Augusto Dos SantosJosé Luiz PedrosoOrlando Grazianni Povoas BarsottiniRoberta Arb SabaHenrique Ballalai FerrazFernando Regla VargasGabriel Vasata FurtadoMarcia Polese-BonattoLuiza Paulsen RodriguesLucas Schenatto SenaCarmen Regla VargasMaria-Luiza Saraiva-PereiraLaura Bannach JardimRede NeurogenéticaPublished in: Arquivos de neuro-psiquiatria (2020)
Although valine levels were lower in HD carriers and were related to BMI losses observed in pre-symptomatic individuals, none of these metabolites seem to be biomarkers for HD.